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Special Design for Organic Intermediate - L-Phenylalanine CAS:63-91-2 99% White powder – XD BIOCHEM

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Special Design for Organic Intermediate - L-Phenylalanine CAS:63-91-2 99% White powder – XD BIOCHEM Detail:

Catalog Number XD90317
Product Name L-Cysteine hydrochloride anhydrous
CAS 63-91-2
Molecular Formula C9H11NO2
Molecular Weight 165.19
Storage Details Ambient
Harmonized Tariff Code 29224985

 

Product Specification

Appearance White crystalline powder
Assay 99%
Specific rotation -20.4 to -35.2
Heavy metals <0.002%
Lead <10mg/kg
pH 5.4 – 6
Loss on Drying <0.40%
Residue on Ignition <0.10%

 

In maple syrup urine disease (MSUD), branched-chain L-amino (BCAA) and 2-oxo acids (BCOA) accumulate in body fluids owing to an inherited deficiency of branched-chain 2-oxo acid dehydrogenase complex activity. In MSUD, little information is available on the significance of urinary disposal of branched-chain compounds. We examined the renal clearance of leucine, valine, isoleucine and alloisoleucine, and their corresponding 2-oxo acids 4-methyl-2-oxopentanoate (KIC), 3-methyl-2-oxobutanoate (KIV), (S)-(S-KMV), and (R)-3-methyl-2-oxopentanoate (R-KMV), using pairs of plasma and urine samples (n = 63) from 10 patients with classical MSUD. The fractional renal excretion of free BCAA was in the normal range (< 0.5%) and independent of the plasma concentrations. The excretion of bound (N-acylated) BCAA was normal and not significantly dependent on the BCAA plasma concentrations. The fractional renal excretion of BCOA was in the order KIC << KIV < R-KMV < or = S-KMV (range (%): KIC 0.1-25; KI V 0.14-21.3; S-KMV 0.26-24.6; R-KMV 0.1-35.9), significantly correlated with the KIC plasma concentrations, and generally higher than that of the related BCAA. The results show that the renal excretion of free BCAA as well as of the acylated derivatives is negligible. The renal excretion of BCOA, however, to some extent counteracts increases in BCAA concentrations and thus contributes to the lowering of total BCAA pools in MSUD.

 


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We are experienced manufacturer. Wining the majority of the crucial certifications of its market for Special Design for Organic Intermediate - L-Phenylalanine CAS:63-91-2 99% White powder – XD BIOCHEM , The product will supply to all over the world, such as: Greece, Romania, Germany, All styles appear on our website are for customizing. We meet up to personal requirements with all products of your very own styles. Our concept is to help presenting the confidence of each buyers with the offering of our most sincere service, and the right product.
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    Special Design for Organic Intermediate - L-Phenylalanine CAS:63-91-2 99% White powder – XD BIOCHEM